Juvenile Paget’s disease in a 12-year-old Nigerian adolescent: a case report
DOI:
https://doi.org/10.30442/Keywords:
Adolescents, Children, Hypercalcaemia, Hypophosphataemia, Paget’s diseaseAbstract
Summary
Paget’s disease (PD) is a skeletal growth disorder characterised by highly elevated bone turnover and fast skeletal remodelling. Typically, PD is a rare disease, and it develops in the later stages of life, whereas Juvenile PD is ultra-rare. We report this 12-year-old female adolescent who presented with clinical, biochemical and radiological features that are in keeping with those of PD. Patient has been commenced on Zoledronic acid injection and outpatient follow-up appropriately. The case is being reported to show that PD, even though rare, does occur in Nigerian children, and clinicians need to be aware so that they can have a high index of suspicion when a similar presentation is encountered in clinical practice.
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